Sheffield Molecular Genetics Service

Address

Sheffield Children’s NHS Foundation Trust

Western Bank

Sheffield

S10 2TH, UK

Contact 1

Dr Ann Dalton

Contact 2

Joanne Martindale

Contact 3

Anne Goodeve

Telephone 1

+44 (0)114 271 7004

Telephone 2

+44 (0)114 271 7003

Telephone 3

+44 (0)114 271 7005

Fax:

 

Email 1

Molecular.Genetics@sch.nhs.uk

Email 2

Molecular.Genetics@sch.nhs.uk

Email 3

Molecular.Genetics@sch.nhs.uk

Home page

http://www.shefflab.co.uk

 

 

Services offered: 07/06/2007 AG update

Disease

OMIM

UKGTN service*

Acute myeloid leukaemia screen (AML1-ETO, CBFB-MYH11) 133435,121360/160745 No
Acute promyelocytic leukaemia screen (PML-RARA) 102578, 180240 No
Amyotrophic Lateral Sclerosis 1 (SOD1) 105400 No
Androgen Insensitivity Syndrome (CAIS/PAIS/MAIS) 300068 No

Antithrombin deficiency (SERPINC1)

107300

No

ApoE (E2 allele for Hyperlipidemia Type III only) 107741 No
BCR-ABL 151410,189980,#608232 No
BCR-ABLQ (Quantitative) 151410,189980,#608232 No
CADASIL 125310 No

Cerebellar Ataxias, DRPLA, Friedreich ataxia, SCA1, SCA2, SCA3, SCA6, SCA7

125370, 229300, 164400, 183090, 109150, 183086, 164500

Yes
Carnitine Acylcarnitine Translocase (CACT) 212138 No
Carnitine Palmitoyl Transferase Type II (CPT2) 255110, 600649, 608836 No
Chimerism studies following bone marrow transplantation   No
CPEO 157640 Yes
Cystic Fibrosis (CF) 219700 No
Dystrohia Myotonica 1 160900 Yes
Early Onset Primary Dystonia (DYT1) 128100 Yes
Ehlers-Danlos syndrome, Type IV 130050 No

Factor XI deficiency (F11)

264900

No

Familial Adenomatous Polyposis, Gardner syndrome, Turcots syndrome, Hereditary Desmoid disease (APC) 175100, 175100, 276300, 135290 No
Fragile X syndrome 309550 Yes
Fructose-1,6-Bisphosphatase (FBP1) 229700 No
Gilbert disease 143500 No
Glutaric Acidaemia Type I (GA1) 231670 No
Glycogen Storage Disease Type 0 (GSD0) 240600 No
Glycogen Storage Disease Type Ia (GSD1a) 232200 No
Glycogen Storage Disease Type Ib (GSD1b) 602671 No
Glycogen Storage Disease Type II (GSD2) 232300 No
Glycogen Storage Disease Type III (GSD3) 232400 No
Glycogen Storage Disease Type IV (GSD4) 232500 & 263570 No
Glycogen Storage Disease Type V (GSD5) 232600 No
Glycogen Storage Disease Type VI (GSD6) 232700 No
Glycogen Storage Disease Type VII (GSD7) 232800 No
Glycogen Storage Disease Type IX (GSD8) 306000, 172490 & 172470 No
GTP-cyclohydrolase I-deficient autosomal dominant dopa-responsive dystonia (GCH1) 233910 Yes

Haemochromatosis (HFE)

235200

No

Haemophilia A (F8)

306700

Yes

Haemophilia B (F9)

306900

Yes

Hereditary Non-Polyposis Colorectal Cancer (HNPCC) 120435, 609310 No
Hereditary Spastic Paraplegia 3 (SPG3A) 182600 No
Hereditary Spastic Paraplegia 4 (SPG4) 182601 Yes
Huntington Disease 143100 Yes
Ig and TCR clonality 147100,186970,186930 No
Long Chain Hydroxyl-CoA-Dehydrogenase deficiency (LCHAD) 609016 No
Kearns-Sayre syndrome 530000 Yes
Leber Optic Atrophy 535000 Yes
Leigh syndrome 256000 Yes
MELAS 540000 Yes
MERRF 545000 Yes
NARP 551500 Yes
Medium Chain Acyl-CoA-Dehydrogenase deficiency (MCAD) 201450 No
Methylentetrahydrofolate Reductase deficiency (MTHFR) 236250 No
Minimal residual disease (MRD) in acute lymphoblastic leukaemia (ALL)   No
Myeloproliferative disorders (MPD) JAK2 147796 No
Multiple Endocrine Neoplasia type 1 (MEN1) 131100 No
Multiple Endocrine Neoplasia type 2, familial medullary thyroid cancer (RET) 171400, 162300, 155240 No
Multiple Colorectal Adenomas (MYH) 608456 No
Osteogenesis imperfecta type I 166200 No
Osteogenesis imperfecta type II 166210 Yes
Osteogenesis imperfecta type III 259420 Yes
Osteogenesis imperfecta type IV 166220 Yes
Osteogenesis Imperfecta Autosomal Recessive (CRTAP) 610854, 610682 No
Osteogenesis Imperfecta Autosomal Recessive (LEPRE1) 610915 No

Protein C deficiency (PROC)

176860

No

Protein S deficiency (PROS1)

176880

No

Pseudoxanthoma Elasticum (PXE) 264800 No
SBMA (Kennedy disease) 313200 Yes
SMA 253300 Yes
Tyrosine hydroxylase-deficient autosomal recessive dopa-responsive dystonia 605407 Yes
Wilms Tumour,Denys Drash syndrome, Frasier syndrome,Mesangial Sclerosis (WT1) 194070,194080, 256370, 256370 No
Very Long Chain Acyl-CoA-Dehydrogenase deficiency (VLCAD) 201475 No
Wilson Disease 277900 No

von Willebrand disease (VWF)

193400,  #277480

No

X-linked Adrenoleukodystrophy (X-ALD) 300100 No

* Services offered outside main commissioning area geographical boundaries under the UK specialist Genetic Testing Network - enquire to the laboratory on costs.

*Services offered outside main commissioning area geographical

boundaries under the UK specialist Genetic Testing Network - enquire

to the laboratory on costs.