Regional Genetics Service

Address

East Anglian Medical Genetics Service

Molecular Genetics, Box 158

Level 6, Addenbrooke's Treatment Centre

Addenbrooke's Hospital

Cambridge CB2 0QQ

Contact 1

 Becky Treacy

Contact 2

 Dr Joanne Whittaker

Contact 3

 

Telephone 1

 01223 348866

Telephone 2

 01223 348801

Fax:

 01223 348870

Email 1

 becky.treacy@addenbrookes.nhs.uk

Email 2

 joanne.whittaker@addenbrookes.nhs.uk

Email 3

 

Home page

 www.addenbrookes.org.uk/moleculargenetics

 

 

Services offered: 17/04/08 update

Disease

OMIM

UKGTN service*

Allan Herndon Dudley (SLC16A2/MCT8)

300523

 YES

Androgen Insensitivity syndrome (AR)

300068

 YES

Angelman syndrome

105830

 

Breast/Ovarian cancer (BRCA1&2)

600185

 

Cystic fibrosis (CFTR)

219700

 

Distal Renal Tubular Acidosis, autosomal dominant (SLC4A1)

179800

YES

Donohue syndrome (INSR)

246200

 

Dentatorubral-Pallidoluysian atrophy (DRPLA)

125370

 

Duchenne/Becker muscular dystrophy (dystrophin)

310200

 

Dysalbuminaemic hyperthyroxinaemia, familial (albumin, ALB)

103600

 

Emery Dreifuss muscular dystrophy, X-linked (EDMD)

310300

YES

Familial adenomatous polyposis coli (APC)

175100

 

Familial juvenile hyperuricemic nephropathy (UMOD)

162000

YES

Focal & segmental Glomerulosclerosis (ACTN4)

603278

 

Fragile X disease (FMR1)

309550

 

Fragile X associated tremor ataxia (FMR1)

300623

 

Friedreich ataxia (FXN)

229300

 

Frontotemporal dementia with Parkinsonism-17 (MAPT/GRN)

600274

YES

Gitelman syndrome (SLC12A3)

263800

YES

Glucorticoid-remediable aldosteronism (CYP11B1/2)

103900

 

Gonadal dysgenesis (SRY)

480000

 YES

Haemochromatosis (HFE)

235200

 

Hereditary fructose intolerance (Aldolase B)

229600

 

Hereditary Non Polyposis Colon Cancer  (MSH2 and MLH1)

114500

 

Huntington disease

143100

 

Incontinentia Pigmenti type II (NEMO)

308300

YES

Liddle syndrome

(SCNN1B, SCNN1G)

177200

 YES

Medium chain acyl CoA dehydrogenase deficiency (MCADD)

607008

 

Medullary cystic kidney disease (UMOD)

603860

 YES

Myotonic dystrophy type 1 (DM1)

160900

 

Polycystic kidney disease, AD

(PKD2)

173910

 

Prader Willi syndrome

105830

 

Rabson Mendenhall syndrome (INSR)

262190

 

Retinoschisis, X-linked (RS1)

312700

YES

Spino and bulbar muscular atrophy, X linked (SMAX1)

313200

 

Spinocerebellar ataxia (SCA1, SCA2, SCA3, SCA6, SCA7, SCA17)

164400, 183090, 109150, 183086, 164500, 607136,

 

Stickler syndrome (COL2A1, COL11A1, COL11A2)

108300, 604841, 184840

 

Thyroid hormone resistance (THRbeta)

190160

 

Tuberous sclerosis (TSC1 and TSC2)

191100, 191092

 YES

Von Hippel Lindau disease

193300

 YES

 

 

 

 

 

 

 

 

 

 

 

 

*Services offered outside main commissioning area geographical

boundaries under the UK specialist Genetic Testing Network - enquire to the laboratory on costs.